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Porphyria
Porphyria
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Overview
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Porphyrias
(9)
Porphyria cutanea tarda
Acute intermittent porphyria
Variegate porphyria
Hepatic porphyria
Hepatoeryt- hropoietic porphyria
Hepatoeryt- hropoietic porphyria
Erythropoietic porphyria
ALAD porphyria
Hereditary coproporphyria
Erythropoietic protoporphyria
more...
Skin conditions resulting from errors in metabolism
(86)
Congenital erythropoietic porphyria
Phenylketonuria
Acute intermittent porphyria
Adrenoleuk- odystrophy
Alkaptonuria
Alkaptonuria
Amyloid purpura
Amyloidosis
Apolipoprotein B deficiency
B-mannosidase deficiency
CADASIL syndrome
Calcinosis cutis
Carotenosis
Cerebrotendineous xanthomatosis
Citrullinemia
Combined hyperlipidemia
Diabetic bulla
Diabetic cheiroarthropathy
Diabetic dermadrome
Diabetic dermopathy
Dystrophic calcinosis cutis
Eruptive xanthoma
Erythropoietic porphyria
Erythropoietic protoporphyria
Fabry disease
Familial apoprotein CII deficiency
Familial dysbetalip- oproteinemia
Familial hypertrigl- yceridemia
Farber disease
Fucosidosis
Gaucher's disease
Gout
Hartnup disease
Hepatoeryt- hropoietic porphyria
Hereditary coproporphyria
Heredofamilial amyloidosis
Hunter syndrome
Hurler syndrome
Hyaluronidase deficiency
Iatrogenic calcinosis cutis
Idiopathic scrotal calcinosis
Lafora disease
Lesch–Nyhan syndrome
Lichen amyloidosis
Limited joint mobility
Lipoprotein lipase deficiency
Macular amyloidosis
Medication-induced hyperlipop- roteinemia
Metastatic calcinosis cutis
Morquio syndrome
Myxedema
Necrobiosis lipoidica
Niemann–Pick disease
Nodular amyloidosis
Nodular xanthoma
Normolipop- roteinemic xanthomatosis
Ochronosis
Osteoma cutis
Palmar xanthoma
Porphyria cutanea tarda
Primary cutaneous amyloidosis
Primary systemic amyloidosis
Prolidase deficiency
Pseudoporphyria
Secondary cutaneous amyloidosis
Secondary systemic amyloidosis
Sialidosis
Sitosterolemia
Subepidermal calcified nodule
Tangier disease
Transient erythroporphyria of infancy
Traumatic calcinosis cutis
Tuberoeruptive xanthoma
Tumoral calcinosis
Urbach–Wiethe disease
Variegate porphyria
Verruciform xanthoma
Waxy skin
Xanthelasma
Xanthoma
Xanthoma diabeticorum
Xanthoma planum
Xanthoma striatum palmare
Xanthoma tendinosum
Xanthoma tuberosum
Xanthomatosis
Xanthomatous biliary cirrhosis
more...
Genetic disorders
(13)
Lucey-Driscoll syndrome
Rotor syndrome
Familial mediterranean fever
Hereditary disease
Crigler-najjar syndrome
Crigler-najjar syndrome
Porphyria cutanea tarda
Acute intermittent porphyria
Variegate porphyria
Congenital erythropoietic porphyria
ALAD porphyria
Hereditary coproporphyria
Erythropoietic protoporphyria
Phenylketonuria
more...
Gastroenterology
Cholestatic
Iron overload
Abdominal pain
Familial mediterranean fever
Hematology
Erythrocyte
Iron overload
Diseases and disorders
(30)
Porphyria congenital erythropoietic
Porphyria hereditary coproporphyria
Porphyria ala-d
Protoporphyria
Post-infectious glomerulonephritis
Post-infectious glomerulonephritis
Pseudochol- inesterase deficiency
Photosensitive epilepsy
Dehydratase deficiency
Hereditary hyperbilirubinemia
Metabolic disorders
Peripheral Neuropathies
Progressive osseous heteroplasia
Bullous pemphigoid
Chloasma
Argyria
Anemias
Heavy metal poisoning
Poliomyelitis
Porphyria cutanea tarda
Acute intermittent porphyria
Variegate porphyria
Congenital erythropoietic porphyria
Hepatoeryt- hropoietic porphyria
Hereditary coproporphyria
Lucey-Driscoll syndrome
Rotor syndrome
Familial mediterranean fever
Cholestatic
Phenylketonuria
Iron overload
more...
Tetrapyrroles
(38)
Heme
Hydroxymethylbilane
Porphyrins
Protoporphyrin
Protoporphyrin IX
Protoporphyrin IX
Bilin (biochemistry)
Bilirubin
Bilirubin (data page)
Biliverdin
Chlorophyll
Chlorophyll a
Chlorophyll b
Chlorophyll c1
Chlorophyll c2
Chlorophyll d
Chlorophyllin
Coproporphyrinogen III
Corrin
Corrole
Heme C
Heme a
Heme b
Heme o
Phycobilin
Phycocyanobilin
Phycoerythrobilin
Phycoerythrocyanin
Phycourobilin
Porphin
Talaporfin
Temoporfin
Tetraphenylporphine sulfonate
Tetrapheny- lporphyrin
Tetrapyrrole
Urobilin
Urobilinogen
Uroporphyrinogen III
Zinc protoporphyrin
more...
Biomolecules
Uroporphyrinogen
Aminolevulinic acid
Porphyrins
Heme
Metabolism
Porphobilinogen
Heme metabolism intermediates
Porphyrins
Metabolic disorders
Kings of Hanover
George IV of Great Britain
George iii
Ernest Augustus I of Hanover
George V of Hanover
William IV of the United Kingdom
EC number
Uroporphyrinogen decarboxylase
Porphobilinogen deaminase
Protoporphyrinogen oxidase
Coproporphyrinogen oxidase
ALA dehydratase
Ferrochelatase
Uroporphyrinogen III synthase
Symptoms
(8)
Premenstrual tenderness and swelling
Back pain
Blistering
Electrolyte imbalances
Rash
Rash
Shock
Sensitivity to light
Abdominal pain
more...
Signs and tests
(9)
Arterial blood gas
Blood urea nitrogen
Creatinine
Enzyme assay
PROTO blood test
PROTO blood test
Renal function
Serum potassium
Tachycardia
Urinalysis
more...
See also
(20)
Cutaneous porphyria
Amanita porphyria
Porphyria's Lover
Heme arginate
Neepawa, Manitoba
Neepawa, Manitoba
ALA dehydratase
Erythropoietic
Pseudo-ainhum
Palm Beach Gardens, Florida
Ferrochelatase
My Last Duchess
PPOX
Alad
Hematin
Porphyrin metabolism
Robert Browning
Analgesic
Carbohydrate
Coma
Gallstone
more...
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