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Hyper-igm Syndromes
Hyper-IgM syndromes
Overview
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Related in the Kosmos
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Genetic disorders
(11)
Zap70 deficiency
Myeloperoxidase deficiency
ICF syndrome
Mevalonic aciduria
Omenn syndrome
Omenn syndrome
Nezelof syndrome
Purine nucleoside phosphorylase deficiency
WHIM syndrome
Adenosine deaminase deficiency
22q11.2 deletion syndrome
Ataxia telangiectasia
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Immune system
Immune disorders
Immunoglobulin
IgM
Myeloperoxidase deficiency
ICF syndrome
Immunology
Myeloperoxidase deficiency
ICF syndrome
IgM
Diseases and disorders
(14)
Complement 2 deficiency
Heavy chain disease
IgM deficiency
Immunoproliferative
Angioedema
Angioedema
Zap70 deficiency
Myeloperoxidase deficiency
Mevalonic aciduria
Omenn syndrome
Nezelof syndrome
Purine nucleoside phosphorylase deficiency
Adenosine deaminase deficiency
22q11.2 deletion syndrome
Ataxia telangiectasia
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Immune system disorders
Immunodeficiency
Zap70 deficiency
Myeloperoxidase deficiency
22q11.2 deletion syndrome
Autosomal recessive disorders
Zap70 deficiency
ICF syndrome
Mevalonic aciduria
Omenn syndrome
Nezelof syndrome
Purine nucleoside phosphorylase deficiency
Adenosine deaminase deficiency
Noninfectious immunodeficiency-related cutaneous conditions
(26)
22q11.2 deletion syndrome
Bare lymphocyte syndrome
Cartilage–hair hypoplasia
Chediak–Higashi syndrome
Chronic granulomatous disease
Chronic granulomatous disease
Common variable immunodeficiency
Complement deficiency
Graft-versus-host disease
Griscelli syndrome
Hyperimmunoglobulin E syndrome
IgM deficiency
Immunodeficiency with hyper-immu- noglobulin M
Leukocyte adhesion molecule deficiency
Myeloperoxidase deficiency
Neutropenia
Nezelof syndrome
Omenn syndrome
Purine nucleoside phosphorylase deficiency
Selective immunoglobulin A deficiency
Severe combined immunodeficiency
Thymoma with immunodeficiency
WHIM syndrome
Wiskott-Aldrich syndrome
X-linked agammaglobulinemia
X-linked hyper-immu- noglobulin M syndrome
X-linked lymphoproliferative disease
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Immunodeficiency
(14)
Primary immunodeficiency
Adenosine deaminase deficiency
Bare lymphocyte syndrome
Common variable immunodeficiency
Complement deficiency
Complement deficiency
HIV
HIV/AIDS
ICF syndrome
Idiopathic CD4+ lymphocytopenia
Immunodeficiency (Acquired immunodeficiency)
Nezelof syndrome
Severe combined immunodeficiency
Severe combined immunodeficiency (non-human)
X-linked severe combined immunodeficiency
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See also
(8)
Hematological malignancy
Cd40 ligand
CD40
Hematology
X linked
X linked
Mutations
B cells
Histology
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