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Familial Hypercholesterolemia
Familial hypercholesterolemia
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Related in the Kosmos
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Lipid disorders
(14)
Blood cholesterol
Cholesterol
Familial combined hyperlipidemia
Hdl cholesterol
Hyperchole- sterolemia
Hyperchole- sterolemia
Hyperlipop- roteinemia
Hypertrigl- yceridemia
LDL-C
Cholesterol Depletion
Hypocholesterolemia
Lipoprotein lipase deficiency
Lipoprotein(a)
Mevalonate inhibition
Triglyceride
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Cardiology
(10)
Atherosclerosis
Intima media thickness
Coronary
Pulse pressure
Hyperchole- sterolemia
Hyperchole- sterolemia
Hyperlipop- roteinemia
LDL-C
Hypertrigl- yceridemia
Familial combined hyperlipidemia
Hdl cholesterol
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Lipids
Lipoproteins
Lipoprotein
Lipid
Triglycerides
Lipid disorders
Coagulation system
(35)
Factor II deficiency
Factor v deficiency
Factor vii deficiency
Factor x deficiency
Antithrombin
Antithrombin
Bone hemostasis
Clot retraction
Coagulation
Cofact
Des-gamma carboxyprothrombin
Factor IX
Factor VIII
Factor XI
Factor XII
Factor XIII
Fibrin
Fibrinogenolysis
Hemostasis
High-molec- ular-weight kininogen
Human Activated Protein C
Medical Laboratory Scientist
Platelet
Platelet activation
Prekallikrein
Protein C
Protein S
Protein Z
Protein Z-related protease inhibitor
Prothrombin complex concentrate
Prothrombinase
Tenase
Thrombomodulin
Tissue factor
Tissue factor pathway inhibitor
Von Willebrand factor
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Genetic disorders
(12)
Fibromuscular dysplasia
Familial spastic paraparesis
Abetalipop- roteinemia
Familial polyposis
Tangier disease
Tangier disease
Adrenoleuk- odystrophy
Homocystinuria
Barraquer-Simons Syndrome
Malonic aciduria
Mitochondrial trifunctional protein deficiency
Familial paroxysmal polyserositis
Hypoalphal- ipoproteinemia
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Skin conditions resulting from errors in metabolism
(87)
Apolipoprotein B deficiency
Familial dysbetalip- oproteinemia
Familial hypertrigl- yceridemia
Xanthelasma
Xanthomas
Xanthomas
Xanthomatosis
Acute intermittent porphyria
Adrenoleuk- odystrophy
Alkaptonuria
Amyloid purpura
Amyloidosis
B-mannosidase deficiency
CADASIL syndrome
Calcinosis cutis
Carotenosis
Cerebrotendineous xanthomatosis
Citrullinemia
Diabetic bulla
Diabetic cheiroarthropathy
Diabetic dermadrome
Diabetic dermopathy
Dystrophic calcinosis cutis
Eruptive xanthoma
Erythropoietic porphyria
Erythropoietic protoporphyria
Fabry disease
Familial apoprotein CII deficiency
Familial combined hyperlipidemia
Farber disease
Fucosidosis
Gaucher's disease
Gout
Gunther disease
Hartnup disease
Hepatoeryt- hropoietic porphyria
Hereditary coproporphyria
Heredofamilial amyloidosis
Hunter syndrome
Hurler syndrome
Hyaluronidase deficiency
Iatrogenic calcinosis cutis
Idiopathic scrotal calcinosis
Lafora disease
Lesch–Nyhan syndrome
Lichen amyloidosis
Limited joint mobility
Lipoprotein lipase deficiency
Macular amyloidosis
Medication-induced hyperlipop- roteinemia
Metastatic calcinosis cutis
Morquio syndrome
Myxedema
Necrobiosis lipoidica
Niemann–Pick disease
Nodular amyloidosis
Nodular xanthoma
Normolipop- roteinemic xanthomatosis
Ochronosis
Osteoma cutis
Palmar xanthoma
Phenylketonuria
Porphyria
Porphyria cutanea tarda
Primary cutaneous amyloidosis
Primary systemic amyloidosis
Prolidase deficiency
Pseudoporphyria
Secondary cutaneous amyloidosis
Secondary systemic amyloidosis
Sialidosis
Sitosterolemia
Subepidermal calcified nodule
Tangier disease
Transient erythroporphyria of infancy
Traumatic calcinosis cutis
Tuberoeruptive xanthoma
Tumoral calcinosis
Urbach–Wiethe disease
Variegate porphyria
Verruciform xanthoma
Waxy skin
Xanthoma diabeticorum
Xanthoma planum
Xanthoma striatum palmare
Xanthoma tendinosum
Xanthoma tuberosum
Xanthomatous biliary cirrhosis
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Hepatology
Cholestyramine
Transaminase
Xanthomas
Xanthelasma
Congenital disorders
Fibrodysplasia ossificans progressiva
Funnel chest
Genetic disorders
Lipoproteins
(11)
Apolipoproteins
Chylomicrons
VLDL
Braun's lipoprotein
Hdl cholesterol
Hdl cholesterol
Intermedia- te-density lipoprotein
LDL-C
Lipid anchored protein
Lipoprotein
Lipoprotein(a)
Lipoprotein-X
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Hypolipidemic agents
(20)
Ezetimibe
Fibrates
Lipid-lowering drugs
Mipomersen
Statins
Statins
Torcetrapib
AEGR-733
Acipimox
Anti-cholesterol
ApoA-1 Milano
Benfluorex
Bile acid sequestrant
Cholesterol absorption inhibitor
Cholestyramine
Colesevelam
Lapaquistat
Magnesium pyridoxal 5-phosphate glutamate
Meglutol
Niacin
Phytosterol
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Statins
(16)
Atorvastatin
Fluvastatin
HMG-CoA reductase inhibitors
Lovastatin
Pravastatin
Pravastatin
Rosuvastatin
Caduet
Cerivastatin
Cholesterol Depletion
Ezetimibe/- simvastatin
Mevalonate inhibition
Mevastatin
Pitavastatin
Scandinavian Simvastatin Survival Study
Simvastatin
Statin development
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Apolipoproteins
(14)
Apolipoprotein A-I
Apolipoprotein B
Apolipoprotein E
APOA4
APOA5
APOA5
Apolipoprotein
Apolipoprotein A2
Apolipoprotein C1
Apolipoprotein C2
Apolipoprotein C3
Apolipoprotein C4
Apolipoprotein D
Apolipoprotein H
Lipoprotein(a)
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Symptoms
Fast breathing
Angina
Coronary artery disease
Obesity
Xanthomas
Low-density lipoprotein
Cholesterol
Diseases and disorders
(29)
Fasciitis, necrotizing
Floppy mitral valve
Fibromyoma
Fish tapeworm
Defective apolipoprotein b-100
Defective apolipoprotein b-100
Rhabdomyolysis
Myopathy
Scorbutic
Lipoprotein disorder
Hyperchole- sterolemia autosomal dominant
Peripheral angiopathies
Factor vii deficiency
Fibromuscular dysplasia
Fast breathing
Hyperlipop- roteinemia
Xanthomas
Familial dysbetalip- oproteinemia
Familial spastic paraparesis
Fibrodysplasia ossificans progressiva
Factor x deficiency
Factor v deficiency
Abetalipop- roteinemia
Familial polyposis
Tangier disease
Homocystinuria
Malonic aciduria
Mitochondrial trifunctional protein deficiency
Funnel chest
Familial paroxysmal polyserositis
more...
Treatment
Atherosclerotic heart disease
Bile
Fat
Niacin
See also
(20)
Fenestrations
LDL receptor
Heterozygous
Homozygote
Fibrosing alveolitis
Fibrosing alveolitis
HMG CoA reductase
Apob
National Cholesterol Education Program
Simvastatin
Homozygous
Dyslipidemia
Acyl CoA dehydrogenase
LDL apheresis
Familial
Ezetimibe/- simvastatin
Isis Pharmaceuticals
Mibefradil
Lipoprotein lipase
Mg/dl
Enzyme
more...
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