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Epidermolytic Hyperkeratosis
Epidermolytic hyperkeratosis
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Genodermatoses
(157)
Bloom syndrome
Congenital ichthyosiform erythroderma
Dermatopathia pigmentosa reticularis
Epidermolysis bullosa dystrophica
Epidermolysis bullosa simplex
Epidermolysis bullosa simplex
Familial cutaneous papillomatosis
Harlequin type ichthyosis
Hay-Wells syndrome
Ichthyoses
Ichthyosis bullosa of siemens
Ichthyosis lamellaris
Ichthyosis vulgaris
Kindler syndrome
Lelis syndrome
Meleda Disease
Naegeli syndrome
X-linked ichthyosis
Zunich Kaye syndrome
18q deletion syndrome
Acrocephal- osyndactylia
Acrodermatitis enteropathica
Acrokeratosis verruciformis
Adams–Oliver syndrome
Adducted thumbs syndrome
Albright's hereditary osteodystrophy
Apert syndrome
Aplasia cutis congenita
Arrhythmogenic right ventricular dysplasia
Ataxia telangiectasia
Atrichia with papular lesions
Atrophodermia vermiculata
Autoimmune polyendocr- inopathy–candidiasis–ectodermal dystrophy syndrome
BIDS syndrome
Bart syndrome
CHILD syndrome
Cardiofaci- ocutaneous syndrome
Cartilage–hair hypoplasia
Carvajal syndrome
Chondrodysplasia punctata
Cicatricial junctional epidermolysis bullosa
Clouston's hidrotic ectodermal dysplasia
Cockayne syndrome
Conradi–Hünermann syndrome
Costello syndrome
Cronkhite-Canada syndrome
Crouzon syndrome
Cutis verticis gyrata
Darier's disease
Disseminated superficial actinic porokeratosis
Disseminated superficial porokeratosis
Dominant dystrophic epidermolysis bullosa
Dyschromatosis universalis hereditaria
Dyskeratosis congenita
Ectodermal dysplasia
Ectodermal dysplasia with corkscrew hairs
Ectrodacty- ly-ectodermal dysplasia-cleft syndrome
Epidermolysis bullosa
Epidermolysis bullosa herpetiformis
Epidermolysis bullosa simplex of Ogna
Epidermolysis bullosa simplex with mottled pigmentation
Epidermolysis bullosa simplex with muscular dystrophy
Erythrokeratodermia variabilis
Focal dermal hypoplasia
Focal palmoplantar keratoderma with oral mucosal hyperkeratosis
Follicular atrophoderma
Franceschetti–Klein syndrome
Freeman-Sheldon syndrome
Generalized atrophic benign epidermolysis bullosa
Generalized epidermolysis bullosa simplex
Generalized trichoepithelioma
Hailey-Hailey disease
Hallermann-Streiff syndrome
Hereditary sclerosing poikiloderma
Hypohidrotic ectodermal dysplasia
IBIDS syndrome
IFAP syndrome
Ichthyosis hystrix
Ichthyosis linearis circumflexa
IgA pemphigus
Incontinentia pigmenti
Incontinentia pigmenti achromians
Junctional epidermolysis bullosa (medicine)
Junctional epidermolysis bullosa gravis
Keratitisâ- €“ichthyosis–deafness syndrome
Keratolytic winter erythema
Keratosis follicularis spinulosa decalvans
Keratosis pilaris
Keratosis pilaris atrophicans faciei
Klinefelter's syndrome
Klippel–Feil syndrome
LEOPARD syndrome
Lentiginosis
Lenz–Majewski syndrome
Linear Darier disease
Linear and whorled nevoid hypermelanosis
Linear porokeratosis
Localized epidermolysis bullosa simplex
Mandibuloacral dysplasia
Marinesco–Sjögren syndrome
McCusick syndrome
Mitis junctional epidermolysis bullosa
Multiple sulfatase deficiency
Netherton syndrome
Neurofibromatosis
Neurofibromatosis type 3
Neurofibromatosis type 4
Neurofibromatosis type I
Neutral lipid storage disease
Noonan syndrome
Odonto–T- richo–Ungual–Digital–Palmar syndrome
PIBI(D)S syndrome
POEMS syndrome
Pachydermo- periostosis
Pachyonychia congenita
Pachyonychia congenita type I
Pachyonychia congenita type II
Papillon–Lefèvre syndrome
Peeling skin syndrome
Pfeiffer syndrome
Pityriasis rotunda
Plaque-type porokeratosis
Polyostotic fibrous dysplasia
Popliteal pterygium syndrome
Porokeratosis
Porokeratosis palmaris et plantaris disseminata
Progeria
Progressive symmetric erythrokeratodermia
Proteus syndrome
Punctate porokeratosis
Rapp–Hodgkin syndrome
Recessive dystrophic epidermolysis bullosa
Refsum's disease
Relapsing linear acantholytic dermatosis
Restrictive dermopathy
Rhizomelic chondrodysplasia punctata
Rombo syndrome
Rothmund–Thomson syndrome
Scleroatrophic syndrome of Huriez
Sjögren–Larsson syndrome
Tooth and nail syndrome
Transient bullous dermolysis of the newborn
Treacher Collins syndrome
Tricho–r- hino–phalangeal syndrome
Tuberous sclerosis
Turner syndrome
Ulerythema
Ulnar–mammary syndrome
Von Hippel – Lindau disease
Watson syndrome
Werner syndrome
Westerhof syndrome
Wilson–Turner syndrome
Wolf–Hirschhorn syndrome
X-linked recessive chondrodysplasia punctata
XXYY syndrome
Xeroderma pigmentosum
Zimmermann–Laband syndrome
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Rare diseases
(18)
Eem syndrome
Barraquer-Simons Syndrome
Gerodermia osteodysplastica
Marshall syndrome
Ichthyosis bullosa of siemens
Ichthyosis bullosa of siemens
Meleda Disease
Lelis syndrome
Congenital ichthyosiform erythroderma
Familial cutaneous papillomatosis
Ichthyosis lamellaris
Zunich Kaye syndrome
Naegeli syndrome
Dermatopathia pigmentosa reticularis
Epidermolysis bullosa simplex
Harlequin type ichthyosis
Kindler syndrome
Hay-Wells syndrome
Bloom syndrome
more...
Keratins
(31)
Cytokeratin
Keratin 1
Keratin 10
Keratin 9
Keratinopathy
Keratinopathy
Type I keratin
Type II keratin
Beta-keratin
Hair keratin
Keratin 12
Keratin 13
Keratin 14
Keratin 15
Keratin 16
Keratin 17
Keratin 18
Keratin 19
Keratin 20
Keratin 21
Keratin 2A
Keratin 3
Keratin 4
Keratin 5
Keratin 6A
Keratin 6B
Keratin 6C
Keratin 7
Keratin 8
Tonofibril
Type I hair keratin
Type II hair keratin
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Syndromes
(12)
Laminopathy
Buschke-Ollendorff syndrome
Ehlers Danlos Syndrome
Alport syndrome
Lelis syndrome
Lelis syndrome
Eem syndrome
Barraquer-Simons Syndrome
Marshall syndrome
Zunich Kaye syndrome
Naegeli syndrome
Hay-Wells syndrome
Bloom syndrome
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Papulosquamous hyperkeratotic skin diseases
Erythroderma
Palmoplantar keratoderma
Meleda Disease
Familial cutaneous papillomatosis
Kindler syndrome
Autosomal recessive disorders
(9)
Meleda Disease
Congenital ichthyosiform erythroderma
Eem syndrome
Gerodermia osteodysplastica
Ichthyosis lamellaris
Ichthyosis lamellaris
Zunich Kaye syndrome
Harlequin type ichthyosis
Kindler syndrome
Bloom syndrome
more...
Congenital disorders
Achondrogenesis type 2
Bethlem myopathy
Congenital malformations
Buschke-Ollendorff syndrome
Ehlers Danlos Syndrome
Dermatologic terminology
Hyperkeratosis
Genodermatosis
Skin disorder
Bullous
Human body
Subcutaneous tissue
Keratinocytes
Keratinopathy
See also
(20)
Diseases and disorders
Schmid metaphyseal chondrodysplasia
Scleroprotein
Pelger-Huet anomaly
Nevus flammeus nuchae
Nevus flammeus nuchae
Autosomal dominant
Autosomal recessive
Hypochondrogenesis
Central American Integration System
Montmorillonite
Steatocystoma multiplex
J. Invest. Dermatol.
Epidermis (skin)
Isotretinoin
Meesmann juvenile epithelial corneal dystrophy
Mutations
James B. Longley
Birthmarks
ROOP
Integument
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